|
NR. 3/2005
|
|
|
|
|
|
|
|
|
Nietypowa dystrofia
siatkówki z nadnormalnym elektroretinogramem
Atypical Retinal Dystrophy with Supernormal Electroretinogram
Dariusz £±k, Wojciech Lubiński
Katedra i Klinika Okulistyki Pomorskiej Akademii Medycznej w
Szczecinie
Kierownik: prof. dr hab. med. Danuta Karczewicz |
|
|
|
|
|
|
|
| Summary: |
Purpose: To present
a literature review of the atypical cone-rod dystrophy
with supernormal electroretinogram and a case of this
dystrophy diagnosed in our electrophysiological
laboratory.
Material and methods: A routine ophthalmologic
examination, fundus photographs, color vision testing,
fluorescein angiography, white-on white static perimetry
and flash electroretinography (ERG) were performed.
Results: The diagnosis of the atypical retinal
dystrophy with supernormal electroretinogram was
established based on the patient's medical history and
characteristic ERG abnormalities i. e.: in the dark
adapted state – reduced amplitude and significantly
increased latency of the b-wave after single, white
flash stimulation (24dB), supernormal b-wave after
single, white flash stimulation (0 dB); in the light
adapted state – reduced amplitude and increased latency
of the b-wave after single, white flash (0 dB) and
flicker stimulations (30 Hz – 0 dB).
Conclusion: In opposite to many retinal
degenerations where the differential diagnosis may be
performed based on the clinical findings alone, flash
ERG is necessary for diagnosis of this atypical cone-rod
dystrophy. |
| |
|
| Key words: |
Atypical cone-rod
dystrophy, supernormal electroretinogram. |
|
|
|
|
|
|
|
|
