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NR. 1/2006
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Sierpowate
odwarstwienie siatkówki
Congenital Falciform Retinal Detachment
Ewa Wójcik
Klinika Okulistyczna Wojskowego Instytutu Medycznego Centralnego
Szpitala Klinicznego Wojskowej Akademii Medycznej w Warszawie
Kierownik: prof. dr hab. n. med. Andrzej Stankiewicz |
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| Summary: |
This article concerns less
known clinical entity described as congenital falciform
retinal detachment. Described case shows falciform fold
running in vitreous body, built from double layer retina
supplied by branches of central retinal artery. The
essence of the clinical entity is in disorder of forming
retinal structure. Incoming fold is not folded regularly
built retina, but tissue coming from vitreous body fetal
artery sheath. There is not any fluid between fold and
retinal pigment epithelium. In most cases patients still
have stable (more or less) visual acuity (it depends on
geographical course of fold as well as coexisting
anomalies in the eyeball).
Apposition of the retina by operational trial has no
chance for success. However, there are cases when
surgical intervention is justified. In Norrie's disease,
where AVR coexists with CNS injury and organ of hearing,
sometimes vitreous hemorrhage occurs. Surgical
intervention allows eyeball preservation, unfortunately
without visual function improvement – in case of
treatment cessation it results in neovascularization (iris,
irido-corneal angle, vitreoretinal traction creation),
posterior adhesions arise, anterior chamber shallows,
retina’s being totally detached and in consequence
eyeball undergoes atrophy. |
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| Key words: |
congenital falciform fold,
retinal dysplasia, Norrie’s disease. |
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