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NR. 1/2009
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Jaskra w zespole
Sturge’a–Webera u dzieci i młodzieży
Glaucoma in the Sturge–Weber Syndrome in Children and
Adolescents
Mirosława Grałek1,2,
Beata Kocyła-Karczmarewicz1, Anna Niwald2
1 Klinika Okulistyki Instytutu „Pomnik – Centrum
Zdrowia Dziecka” w Warszawie
Kierownik: prof. dr hab. n. med. Mirosława Grałek
2 Klinika Okulistyki Dziecięcej Katedry Pediatrii
Zabiegowej Uniwersytetu Medycznego w Łodzi
P.o. kierownika: dr n. med. Anna Niwald |
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| Summary: |
The main purpose of this
article is to describe ocular features including
glaucoma associated with Sturge–Weber syndrome and
therapeutic management methods. Weber–Sturge syndrome is
a nonheritable congenital mesodermal phakomatosis with
typical clinical symptoms. There are port- wine stain on
the face and vascular malformations of the leptomeninges
and cerebri, and ocular changes. Ocular involvement can
include glaucoma and vascular malformations of the
conjunctiva, episclera, choroid, and retina. Glaucoma
occurs in 40% of children with Sturge–Weber syndrome.
Glaucoma is the most often and very serious complication
of this disease. The pathogenetic factors are unknown.
The management of glaucoma associates with Sturge–Weber
syndrome is difficult. The therapy include
pharmacological and surgical treatment. |
| Key words: |
phakomatosis, children,
ocular findings, glaucoma, management. |
| Słowa kluczowe: |
fakomatozy, dzieci, zespół
Sturge'a–Webera, leczenie jaskry. |
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