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NR 7-9/2005
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Zespół
Vogta-Koyanagi-Harady u 11-letniej dziewczynki
The Vogt-Koyanagi-Harada
syndrome in 11-year-old girl
Anna Święch-Zubilewicz, Ewa Wróblewska1,
Anna Mańkowska
Z I Kliniki Okulistyki Akademii Medycznej w Lublinie
Kierownik: prof. dr hab. n. med. Zbigniew Zagórski
1Z II Kliniki Okulistyki Akademii Medycznej w
Lublinie
Kierownik: dr hab. n. med. Marek Gerkowicz |
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| Summary: |
Purpose: The
Vogt-Koyanagi-Harada syndrome is an idiopathic,
multisystem disorder which typically affects pigmented
individuals between 20-50 years old. The typical
symptoms include granulomatous panuveitis with
characteristic extraocular dermato-neurological
manifestations. The case of VKH syndrome affecting
Polish girl is very rare.
Case report: A 11-year-old girl had an important
decrease of visual acuity in both eyes (RE 0.1 and LE
0.2), with the presence of bullous serous retinal
detachment in both eyes. Besides, in right eye some
keratic precipitates were noted. The routine laboratory
evaluation failed to provide a diagnosis. The patient
was treated with an intravenous bolus of corticosteroid
therapy and then, high dose of oral prednisone.
Results: After administered therapy the visual
acuity improved rapidly in both eyes (RE 1.0 and LR
0.9), and the exudative retinal detachment resolved.
After 5 months, the patient's examination showed a
sunset glow fundus with several whitish rounded lesions
in peripheral fundus, which is typical for the VKH
syndrome.
Conclusions: The VKH syndrome rarely affects
young children, so the diagnosis may be difficult in the
absence of the typical extraocular manifestations. In
such atypical cases the diagnosis is based on the
clinical evolution of the disease. |
| Słowa kluczowe: |
zespół
Vogta-Koyanagi-Harady, zapalenie błony naczyniowej. |
| Key words: |
Vogt-Koyanagi-Harada
syndrome, uveitis. |
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