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NR 1-3/2008
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Guz rzekomy oczodołu
w przebiegu choroby Ormonda
Orbital pseudotumor due to
Ormond’s disease
Joanna Murawska, Paweł Lipowski, Krystyna
Raczyńska
Z Kliniki Chorób Oczu Akademii Medycznej w Gdańsku
Kierownik: prof. dr hab. n. med. Krystyna Raczyńska |
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| Summary: |
Retroperitoneal fibrosis (RPF)
is characterized by the presence of a fibro-inflammatory
tissue, which usually surrounds the abdominal aorta and
the iliac arteries and extends into the retroperitoneum.
Up to 15% of patients have additional fibrotic processes
outside the retroperitoneum. Retroperitoneal fibrosis is
generally idiopathic, but can also be secondary to the
use of certain drugs, malignant diseases, infections and
surgery. The etiology of idiopathic retroperitoneal
fibrosis, so called „Ormond’s disease”, remains unknown.
In this study we present the 54 years old woman with
orbital pseudotumour of right lacrimal gland associated
with retroperitoneal fibrosis. Diagnosis was confirmed
with computed tomography of abdominal cavity and orbit.
Needle biopsy from the tumour in the orbit revealed only
fibrous tissue with signs of chronic inflammation.
Together with typical findings of an idiopathic
retroperitoneal fibrosis, the final diagnosis of
Ormond’s disease with orbital pseudotumorous fibrosis
was made.
It is important that both, the ophthalmologist and the
urologist are aware of the existence of this association,
so that suitable treatment can be initiated without
delay. |
| Słowa kluczowe: |
choroba Ormonda, guz
rzekomy oczodołu, idopatyczne zwłóknienie
pozaotrzewnowe. |
| Key words: |
idiopathic retroperitoneal
fibrosis, orbital pseudotumor, Ormond’s disease. |
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