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NR 4-6/2008
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Zespół małoocza –
własne doświadczenia w leczeniu 60 pacjentów
Orbitoblepharophimosis
syndrome – own clinical experience in treatment of 60 patients
Kazimierz Kobus, Piotr Wójcicki, Mariusz
Wysocki
Z Kliniki Chirurgii Plastycznej Akademii Medycznej we Wrocławiu
Z Oddziału Chirurgii Plastycznej Specjalistycznego Centrum
Medycznego w Polanicy Zdroju
Kierownik: prof. dr hab. n. med. Kazimierz Kobus |
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| Summary: |
Purpose: The
orbitoblepharophimosis syndrome is an autosomal-dominant
congenital malformation involving the orbitopalpebral
region. The condition is associated with orbital
phimosis, upper eyelid ptosis, epicanthus and
telecanthus.
Material and methods: We retrospectively reviewed
the records of 60 patients with blepharophimosis who
underwent surgery in the Hospital of Plastic Surgery in
Polanica Zdrój from January 1975 to January 2006. The
study population consisted of 23 (38.3%) females and 37
(61.7%) males patients whose age at the time of first
surgical stage ranged from 1 to 48 years (mean 8 years).
Surgical management consisted of epicanthus correction
using modified technique of Mustardé, followed by eyelid
suspension to the frontalis muscle with using temporal
fascia. In patients with orbitoblepharophimosis type II,
correction of the lower lid ectropion and antimongoid
slanting palpebral fissures, were performed before or
after Mustardé procedure.
Results: In our series of 60 patients, good
result of treatment was obtained in 80.1% and
satisfactory in 18.3% of patients. Poor outcome was
obtained only in one patient with orbitoblepharophimosis
type II.
Conclusions: Orbitoblepharophimosis management
should consists of gradual and complex surgical
treatment. During the first stage epicanthus correction
is performed. As a second stage, blepharoptosis is
treated by frontalis suspension technique with using
temporal fascia. |
| Słowa kluczowe: |
zespół małoocza, leczenie
chirurgiczne. |
| Key words: |
orbitoblepharophimosis
syndrome, surgical treatment. |
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